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8 article(s) in the watch · Cancer genetics

MLH1 is a DNA mismatch-repair (MMR) gene. Germline pathogenic MLH1 variants are a major cause of Lynch syndrome (HNPCC), an autosomal-dominant predisposition to colorectal and endometrial cancer, associated with tumour microsatellite instability.

Curated publications

8/10

Clinical and Genetic Characterization of Constitutional MLH1 Promoter Hypermethylation: Implications for Lynch Syndrome Diagnosis.

Lynch syndrome due to constitutional MLH1 promoter hypermethylation

Onco20 May 2026
7/10

The germline MLH1 c.2054 C>T mutation disrupts DNA mismatch repair and is detectable by digital PCR.

Lynch syndrome

Onco16 June 2026
7/10

Gene-specific cancer risks in female Lynch syndrome carriers: A copula-based meta-analysis

Lynch syndrome — gene-specific cancer risks in female carriers

Onco6 May 2026
6/10

Universal Tumor Screening in Colorectal Cancer: Role of MMR Immunohistochemistry for Lynch Syndrome and Early-Onset CRC.

Lynch syndrome — universal tumour screening in colorectal cancer

Onco1 September 2026
6/10

Genetic Landscape of Lynch Syndrome in a High-Risk Serbian Cohort: Predominance of MLH1 Variants and Implications for Risk-Based Testing.

Lynch syndrome

Onco18 August 2026
6/10

Performance of PREMM5, clinical criteria, and immunohistochemistry for MMR proteins in genetic risk assessment of Mexican patients with colorectal cancer.

Lynch syndrome and hereditary colorectal cancer predisposition

Onco11 August 2026
5/10

Mismatch Repair Deficiency in Upper Gastrointestinal and Pancreaticobiliary Cancers: Integrating Multimodal Molecular Data in Clinical Practice.

Lynch syndrome and upper gastrointestinal cancers

Onco15 September 2026
5/10

Real-world uptake of Lynch syndrome testing among patients with mismatch repair-deficient endometrial cancer in Québec

Lynch syndrome — endometrial cancer

Onco8 September 2026

Frequently asked questions

How many Geno'X publications cover the MLH1 gene?+

8 publication(s) on MLH1 have been selected, summarised and scored by Geno'X on a public grading grid (domains: Cancer genetics).